Cor Triatriatum Sinistrum: Classification and Imaging Modalities

REVIEW, Jan 2011, VOL I ISSUE III, ISSN 2042-4884
10.5083/ejcm.20424884.21 , Cite or Link Using DOI
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Pierre Nagib Nassar MD. MSc & Righab Haidar Hamdan MD,

ABSTRACT

Cor Triatriatum Sinister is a rare congenital abnormality, usually diagnosed in childhood; few cases remain asymptomatic and are diagnosed in adulthood. In this review article we focus on classification and etiologies, clinical manifestations, novel diagnostic modalities and treatment of Cor triatriatum Sinister.

INTRODUCTION

Triatrial heart is a rare congenital abnormality, reported by Jeiger at the autopsy, in 0.4% of patients with congenital heart disease (1), and found in less than 0.1% of clinically diagnosed cardiopathies (2). Though it was first described by Church in 1868, as a left atrium divided by an abnormal septum, the name “cor triatriatum” was given by Borst in 1905 (3). It involves usually the left atrium (cor triatriatum sinister) and rarely the right atrium (cor triatriatum dexter), in this review, we will be discussing cor triatriatum sinister (CTS).

No clear difference in the incidence of the disease has been noted among men or women and no related genetic disorders have been described in the literature. The anomaly may be associated with other congenital cardiac lesions in up to 80% of cases in pediatric population, most frequently with ostium secundum atrial septal defect and anomalous pulmonary vein return (4). Other associated lesions are listed in Table 1...